Prof. Sabri Kemahli

Professor of Pediatrics

Bio

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Sabri KEMAHLI CV
CURRICULUM VITAE
 
DR.SABRİ KEMAHLI
 
 
PALCE AND DATE OF BIRTH :       ANKARA, 11.7.1954
MARITAL STATUS :             MARRIED, HAS 2 CHILDREN
FOREIGN LANGUAGES :   ENGLISH, GERMAN
CURRENT POSITION : 

Professor of Pediatrics and Phase III (Clinical Clerkships) Director, College of Medicine, Alfaisal University, Riyadh: Saudi Arabia

CONTACT :
                                         Mobile  :   +90-532 264 55 02, 
                                                              +966-535 238 077
                                                          Home  :      +90-312- 266 33 22
                                                          Work :        +90-312- 595 66 35
                                                      E-mail : kemahli@medicine.ankara.edu.tr ; skemahli@alfaisal.edu
 
EDUCATION AND TRAINING :                                                        

Resident at the Pediatric Hematology Division of Department of Pediatrics, Faculty of Medicine, Ankara University (1988-1989).
Resident in the Department of Pediatrics, Faculty of Medicine, Ankara University (1979-1984). 
Graduated from the Faculty of Medicine, Ankara University in 1978 as M.D.

 
DIPLOMAS AND DEGREES :
Professor of Pediatrics and Ped.Hematology 1997 (Faculty of Medicine, Ankara University)
Pediatric Hematologist- 1991 (Faculty of Medicine, Ankara University)
Associate Professor of Pediatrics- 1989 (Faculty of Medicine, Ankara University)
Pediatrician- 1984 (Faculty of Medicine, Ankara University)
ECFMG-1980
Doctor of Medicine- 1978 (Faculty of Medicine, Ankara University)
 
ACADEMIC APPOINTMENTS:
 
2011-   :           Professor of Pediatrics (Pediastric Hematology), College of Medicine, Al Faisal University, Riyadh, S.Arabia
1997- 2011 :  Professor of Pediatrics (Pediatric Hematology), Faculty of Medicine, Ankara University
1996-2000 and 2005-2008:  Vice Dean (for Education and Academic Affairs), Faculty of Medicine, Ankara University
1997 – 2009: Director, Serpil Akdağ Blood Centre, Ankara University
1999 -  2009:      Faculty member, Department of Medical Education and Informatics, Faculty of Medicine, Ankara University
1989-1997       : Associate Professor of Pediatrics , Faculty of Medicine, Ankara University
1988  – 1989     : Resident at the Pediatric Hematology Division of Department of Pediatrics, Faculty of     Medicine, Ankara University (1988-1989).
1985 – 1988  : Pediatrician at Atatürk Children's Home (Orphanage) of  the Social Services and Child Protection Agency (1985-1988).
1984  –  1985     : Military service at the Department of Pediatrics, Gülhane Military Medical Academy
1979  –  1984    : Resident in the Department of Pediatrics, Faculty of Medicine, Ankara University
 
EXPERIENCE ABROAD:

 ECFMG-IFME Fellow in Medical Education at University of Texas Medical Branch at Galveston, TX,USA (January-September 2000)
Visiting scientist at the Haemophilia Centre and Haemostasis Unit, Royal Free Hospital, London, U.K. (1990).

 
MAIN FIELDS OF INTEREST AND EXPERIENCE: Medical Education, Hemostasis and thrombosis, thalassemia and hemoglobinopathies,  blood banking-transfusion medicine
 
 
 
 
 
MEMBERSHIPS:
International Society of Haematology (ISH)
Association for  Medical Education in Europe (AMEE)
American Society of Hematology (ASH)
International Society on Thrombosis and Haemostasis (ISTH)
Ankara Thalassaemia Society
Turkish Society of Haematology
Blood Banks and Transfusion Society of Turkey
Haemophilia Society (Ankara)
 
ADMINISTRATIVE DUTIES AND RESPONSIBILITIES:
In University:
1996-2000 and 2005-2008:  Vice Dean (for Education and Academic Affairs), Faculty of Medicine, Ankara University
1994-1996 and 2000-2003 : Member, Faculty Academic Board, Ankara University Faculty of Medicine
2003-2005 :  Member, Faculty Administrative Board, Ankara University Faculty of Medicine
1997-2009 :  Director, Serpil Akdağ Blood Centre, Ankara University
1996-2008 :  Member and Chairman, Undergraduate Education Coordination Committee, Ankara University Faculty of Medicine
1996-2000; 2005-2008: Member, Postgraduate Education Coordination Committee, Ankara University Faculty of Medicine
2003-2005   :  Year 3 Undergraduate Education Coordinator, Ankara University Faculty of Medicine
2002-2009 : Member, Educational Methods and Case Development Committee, Ankara University Faculty of Medicine
2002- 2009  : Member, Assessment and Evaluation Committee, Ankara University Faculty of Medicine
2007- 2009   :  Erasmus Coordinator, Ankara University Faculty of Medicine
2005 :         Member, ad hoc Committee for European University Association Self Assessment Report, Ankara University Faculty of Medicine
2008 - 2009    : Member, Bologna Process Coordination Committee, Ankara University
2005- 2010 : Member, Academic Evaluation and Quality Improvement Committee, Ankara University
 
 
Scientific Societies and Groups:
2008 -       : Secretary General, European-African Division, International Society of Hematology
2002 -       : National Councillor,  International Sociaety of Hematology (representing Turkish Society of Hematology)
2007-2011   : Member, Turkish National Accreditation Council for Medical Education; member of Committee for Defining and Developing Standards for Undergraduate Medical Education.
2005- 2007   : Member, Medical Education in EuropeMEDINE) Thematic Network
2007- 2009  : Member, European Pediatric Thematic Network (EUROPET)
2008- 2012  : Member, Medical Education in Europe-2 (MEDINE-2) Thematic Network
2007 - 2008  : President, Turkish Society of Pediatric Hematology
2001- 2007   : Member, Administrative Board, Turkish Society of Pediatric Hematology
2004 - 2010  : Member of Administrative Board, Turkish Society of Medical Education   
2007 - 2008  : Member, European Pediatric Thematic Network (EUROPET)
2004 -            : Member, Board of Trustees, Turkish Blood Foundation
2004 - 2009 : Member, Ministry of Health Blood Services Advisory Board
2004 -  2009  : Member, Ministry of Health Scientific Committee of Blood Centres
2004 - 2009  : Member, Ministry of Health Commission for Hemapheresis and Photopheresis
1996-1997   :  Member,Administrative Board, Ankara Chamber of Physicians
 
 
 
EDUCATIONAL ACTIVITIES
 
A) UNDERGRADUATE
  1.    PBL Facilitator for Year 1, 2 and 3 students (2002-2009)
   2.   Evidence Based Medicine lectures
              -  What is EBM?
               - Professsionalism
   3. Lectures and Bedside training for Year 5 students in Pediatrics Clerkship
                 - Hematological parameters in children
                -  Transfusion in pediatrics
                 - Hemostasis disorders in childrenemaostasis disor5rdersHemostasis disorders in children     
                 -Approach to bleeding patient-clinical presentation
 
 B) POSTGRADUATE
    1. Practical and theoretical training for residents in pediatrics
    2. Practical and theoretical training for residents in pediatric hematology
    3. Blood Bankling and Transfusion Medicine Masters Programme (Programme director)
    4. Medical Education Masters Programme
 
C) CONTINUOUS PROFESSIONAL  DEVELOPMENT
1. Blood Banking and Transfusion Medicine Certificate program coordinator for the Ministry of Health
2. Bedside Transfusion safety training course for nurses ( Ankara University Faculty of Medicine)
3. Problem based learning tutor workshops for the faculty members, Ankara University Faculty of Medicine.  28 workhops (3-day each) for groups of 20-30 between 2001-2008.
4. Assessment and Evaluation workshop for the facultry members. Ankara University Faculty of Medicine)
5. Educational skills workshops ( 5-day workshops to groups of 15 people between 1999-2006)
6. Problem based learning tutor workshops for the faculty members, Alfaisal University College of Medicine (2012)
7. Assessment and Evaluation and OSCE workshops for clinical clerkships staff at King Faisal Specialist Hospital and Research Centre, Riyadh, S. Arabia (2011, 2012)
 
 
 

EDITOR FOR SCIENTIFIC JOURNALS
Tıp Eğitimi Dünyası (“The World of Medical Education”-Turkish Journal of Medical Education) (2009-)    
Çocuk Hematoloji Dergisi (Turkish Journal of Pediatric Hematology)  (2009-   )
 
REFEREE FOR SCIENTIFIC JOURNALS
 
Çocuk Sağlığı ve Hastalıkları Dergisi Turkish Journal of Pediatrics
Turkish Journal of Hematology Medical Teacher Medical Education Online Interdisciplinary Journal of Problem Based Learning
Tıp Eğitimi Dünyası (Turkish Journal of Medical Education)
Çocuk Hematoloji Dergisi (Turkish Journal of Pediatric Hematology)

PUBLICATIONS: A. International SCI Indexed Journals
1. Kemahlı S, Babacan E, Çavdar AO: Cell-mediated immune responses in children with iron deficiency and combined iron and zinc deficiency. Nutrition Research, 8(3), 129-136, 1988.
2. Kemahlı S, Sarp N: The growth and development of children living in residential units (Children’s Homes) in Turkey. Maladjustment and Therapeutic Education, 7:163-168:1989.
3. Canatan D, Erden İ, Aykaç S, Akar N, Kemahlı S, Arcasoy: Doppler colour flow imaging for the evaluation of postsplenectomy portal vein thrombosis in pediatric hematological diseases. Pediatric Hematology and Oncology, 9:297-399, 1992. 
4.Uysal Z, Akar N, Kemahlı S, Dinçer N, Arcasoy A: Desferrioxamine and urinary zinc excretion in b-thalassemia major. Pediatric Hematology  and Oncology, 1257-260, 1993. 
5. Kemahlı S, Goldman E, McCraw A, Jenkins V, Kernoff PBA: Value of DNA analysis with multiple DNA probes for the detection of hemophilia A carriers. Pediatric Hematology and Oncology, 11:55-62, 1994. 
6. Kemahlı S, Canatan D, Uysal Z, Akar N, Uysal Z, Cin Ş, Arcasoy A: DDAVP shortens bleeding time in Bernard-Soulier syndrome. Thrombosis and Haemostasis, 71(5): 675, 1994. 
7. Suskan E, Kemahlı S, Atalay S, Ertogan F, Karademir S: Intracardiac thrombosis associated with acquired protein C deficiency. European Journal of Pediatrics, 153(11): 862-863, 1994. 
8. Kemahlı S, Canatan D, Uysal Z, Akar N, Cin Ş, Arcasoy A: GM-CSF in the tratment of Fanconi’s anaemia. British Journal of Haematology, 87:871-872, 1994. 
9. İnce E, Kemahlı S, Uysal Z, Akar N, Dinçer N, Cin Ş, Arcasoy A: Mild zinc deficiency in preschool children. The Journal of Trace Elements in Experimental Medicine, 7: 135-141, 1995.
10. Yıldırmak Y, Kemahlı S, Akar N, Uysal Z, Cin Ş, Arcasoy A: A case of severe thrombocytopenia due to parvovirus B19 virus. Pediatric Hematology and Oncology, 13:183-185, 1996. 
11.Kemahlı S, Gürman C, Eğin Y, Akar N, Uysal Z, Cin Ş, Arcasoy A: Hypercoagulability in children with thalassemia major. Clinical and Applied Thorombosis/Hemostasis, 3(2): 129-132, 1997. 
12. Kemahlı S, Uysal Z, Canatan D, Akar N, Cin Ş, Arcasoy A: Post-slenectomy thrombosis and haemolytic anaemias. British Journal of Haematogy 97(2): 505, 1997.
13.  Kemahlı S, Alhenc-Gelas M, Gandrille S, Aiach M, Akar N,  Cin Ş: Homozygous Protein C Deficiency With A Double Variant His 202 To Tyr And Ala 346 To Thr. Blood Coagulation and Fibrinolysis, 9:351-354,1998. 
14.  Arcasoy A, Öcal G, Kemahlı S, Berberoğlu M, Yıldırmak Y, Canatan D, Akçurin S, Akar N, Uysal Z, Adıyaman P, Çetinkaya E: Recombinant human growth hormone treatment in children with thalassemia major. Pediatrics International, 41:655-661, 1999. 
15. Dalyan M, Tuncer S, Kemahlı S: Hemophilic arthropathy: evaluation of clinical and radiological characteristics and disability. Turkish Journal of Pediatrics, 42: 205-209, 2000. 
16.  Ekim N, Akar N,  Tutar E, Kemahlı S, Tümer N: Endothelin-1 and von Willebrand Factor in pseudoxanthoma elasticum. Pediatric Nephrology, 14 (8-9): 882-3, 2000. 
17. Yıldırmak Y, Kemahlı S, Dinçer N, Hasanoğlu A, Biberoğlu G, Cin Ş, Arcasoy A: Hyperzincuria and selective amino aciduria in thalassemia. Journal of Trace Elements in Experimental Medicine, 13: 199-204, 2000. 
18. Akar N, Kemahlı S, Deda G, Akar E, Yılmaz E, Uysal Z, Cin Ş: Multiple cerebral emboli in a homozygous b-thalassaemia patient due to factor V 1299 (His-Arg) 4070 A-G mutation. Turkish Journal of Haematology, 17(3): 133-136, 2000.
19. Dalyan M, Tuncer S, Kemahlı S: Hemophilic arthropathy: evaluation of clinical and radiological characteristics and disability. Turkish Journal of Pediatrics, 42: 205-209, 2000.
20. Kemahli S. Clinical teaching and OSCE in pediatrics. Med Educ Online [serial online] 2001;6:10. Available from URL http://www.med-ed-online.org
21.Manco-Johnson MJ, Grabowski EF, Hellgreen M, Kemahli AS, Massicotte MP,  Muntean W, Peters M, Nowak-Göttl U: Laboratory Testing for Thrombophilia in Pediatric Patients. Thrombosis and Haemostasis, 88:155-156, 2002. 
22.  Manco-Johnson MJ, Grabowski EF, Hellgreen M, Kemahli AS, Massicotte MP,Muntean W,Peters M, Schlegel N, Wang M, Nowak-Göttl U. Recommendations for tPA Thrombolysis in Children. Thrombosis and Haemostasis, 88:157-158, 2002. 
23. Onay V, Kavaklı K, Kılınç Y, Gürgey A, Aktuğlu G, Kemahlı S, Özbek U, Çağlayan H: Molecular pathology of haemophilia B in Turkish patients: identifiation of a large deletion and 33 independent point mutations. British Journal of Haematology, 2003; 120:656-659. 
24. Atasay B, Arsan S, Günlemez A, Kemahlı S, Akar N: Factor V Leiden and prothrombin gene 20210A variant in neonatal thromboembolism and in healthy neonates and adults. Study in a single center. Pediatric Hematology and Oncology, 2003; 20: 627-634. 
25. Kemahlı S, Dökmeci F, Palaoğlu Ö, Aktuğ T, Arda B, Demirel-Yılmaz E, Karahan T, Özyurda F, Akan H, Ayhan İH: How we derived a core curriculum: from institutional to national-Ankara University experience. Medical Teacher, 2004; 26: 295-298.  
26. Kavaklı K, Aktuğlu G, Kemahlı S, Devecioğlu O:  Inhibitor screening project for patients with hemophilia in a developing country: Turkey. Haemophilia 2004; 10, (Suppl. 3), 58. 
27. Uçar T, Gürman C, Arsan S, Kemahlı S: Platelet aggregation in term and preterm newborns. Pediatric Hematology and Oncology, 2005; 22:139-145. 
28.İkincioğulları A, Doğu F, Solaz N, Reisli İ, Kemahlı S, Cin Ş, Babacan E: Granulocyte transfusions in children with chronic granulomatous disease and invasive aspergillosis. Therapeutic Apheresis and Dialysis, 2005; 9(2): 137-141.
29.Kemahlı S:Hematology education in a problem-based curriculum. Hematology, 2005;10 Suppl 1:161-163. 
 
30. Kavaklı K, Aktuğlu G, Kemahlı S, Başlar Z, Ertem M, Balkan C, Arr C, Yılmaz Karapınar D,  Bilenoğlu B,  Gülseven M, Gürman C: Inhibitor screening for patients with hemophilia in Turkey. Turk J Hematol 2006;23(1): 25-32
31. Demirören M, Palaoglu, Ö, Kemahlı S, Özyurda F Ayhan HI. Perceptions of students in different phases of medical education of educational
environment: Ankara University Faculty of Medicine. Med Educ Online [serial online] 2008;13:8 doi;10.3885/meo.2008.Res00267Available from http://www.med-ed-online.org
32. Acar A, Kemahlı S, Altunay H, Koşan E, Öncül O, Görenek L, Çavuşlı Ş: HBV,    HCV and HIV seroprevalence among blood donors in Istanbul, Turkey: how effective are the changes in the national blood transfusion policies? Brazilian Journal of  Infectious Diseases 2010;14: 41-46
    33. Acar A, Kemahlı S, Altunay H, Koşan E, Öncül O, Görenek L, Çavuşlu Ş. The significance of repeat testing in Turkish blood donors  screened with HBV,   HCV    and HIV immunoassays and the importance of S/CO ratios in the interpretation of HCV/HIV screening test results and as a determinant for further confirmatory testing. Transfusion Medicine, 2010, 20, 152–159.
 
34. Demirören M, Aytuğ-Koşan AM, Palaoğlu Ö, Aktuğ T, Kemahlı S: Self-perceptions of problem-based curriculum graduates about their professional competency and quality of medical education. Medical Teacher 2010;32(12):1010-1011.
 
35. Sahyoun-Tokan R, Arsan S, Erdeve Ö, Solaz N, Avcı A, Elgün-Ülkar S, Gülyapar E, Üstünyurt Z, Bıyıklı Z, Kemahlı S:  Comparison of stored umbilical cord blood with donated adult blood: a study for transfusion feasiblity. Turk J Hematol , 2012; 29:233-241.
 
B. Publications in refereed National Journals:

Kemahlı S: Yetersiz Beslenmede Bağışıksal Durum. Romatizma, 2(5):139-156, 1978.
Cin Ş, Kemahlı S, Doğu Ü, Demirağ B: Son 10 yılda izlenen ampiyem olgularımız. Ankara Tıp Bülteni, 1(3): 255-164, 1979.
Akar N, Kemahlı S, Abal G: Factors influencing the duration of breast feeding in Ankara. Ankara Tıp Bülteni, 4(3), 201-206, 1982.
Kemahlı S, Oğur G, Turhanoğlu İ, Uluoğlu Ö, Timlioğlu B, Gürel M: Retroperitoneal endodermal sinüs tümörü (sarı kese tümörü). Tümay SB, Cenani A, Yalçın E(ed.):XXI. Türk Pediatri Kongresi . Pediatrik Nöroloji. İstanbul, 5-9 Temmuz 1982. Türk Pediatri Kurumu Yayınları. Özlem Kardeşler Matbaası, İstanbul 1983. s.:531-535.
Kemahlı S, Oğur G, Turhanoğlu İ, Berki  R, Dinçer S, Öcal G, Laleli Y: Bir erkek yalancı hermafroditizm olgusu: psödovaginal perineoskrotal hipospadias. Tümay SB, Cenani A, Yalçın E (ed.): XXI. Türk Pediatri Kongresi. Pediatrik Nöroloji. İstanbul, 5-9 Temmuz 1982. Türk Pediatri Kurumu Yayınları. Özlem Kardeşler Matbaası, İstanbul 1983. s.:349-353.
Kemahlı S, Sarp N: Yuva çocuklarının sağlık sorunlarının sağlık sorunları. Çocuk Hastalıkları Dergisi, 2(3): 155-159, 1987.
Kemahlı S, Evlat edinilmenin çocukta büyümeye etkisi. A.Ü. Tıp Fakültesi Mecmuası, 40(4), 279-284, 1987.
Kemahlı S, Babacan E, Çavdar AO: saf demir eksikliği ile demir-çinko eksikliğinde hücresel bağışıklık. Ulutin O, Kılıçturgay K ve ark. (ed.): Hematoloji-1987-IX. Uycan Basımevi, İstanbul, 1988.s.:571-576.
Kemahlı S, Kunak B, Kantaroğlu N: Bir Çocuk yuvasında HBsAg ve Anti-HBs taraması sonuçları. Çocuk Sağlığı ve Hastalıkları Dergisi, 31:11-116,1988.
Kemahlı S, Gökdoğan S, Bulut B, Arcasoy A: Deniz mavisi histiosit sendromu (Sea-blue histiosit sendromu). A.Ü.Tıp Fakültesi Mecmuası, 43:453-458, 1990.
Bulut B, Kemahlı S, Kanamalı hastalıkların tedavisinde desmopressin kullanımı. Türkiye Klinikleri Tıp Bilimleri Dergisi, 12: 162-171,1992.
Canatan D, Dağdemir A, Kemahlı S, Akar N, Cin Ş, Arcasoy: İmmün trombositopenik purpura (86 olgunun izlem ve tedavisi) . Türkiye Klinikleri Pediatri Dergisi, 1:54-57, 1992.
Canatan D, Uysal Z, Kemahlı S, Akar N, Cin Ş, Arcasoy A: Herediter sferositoz (22 olguda klinik özellikler, komplikasyonlar ve tedavi). A.Ü. Tıp Fakültesi Mecmuası, 46: 101-108, 1993.
Canatan D, Uysal Z, Akar N, Kemahlı S, Cin Ş, Arcasoy A: Akrodermatitis enteropatika. A.Ü. Tıp Fakültesi Mecmuası, 46:677-686, 1993.
Canatan D, Arcasoy A, Öcal G, Tutat E, Akar N, Kemahlı S, Uysal Z, Cin Ş:  Multipl endokrin komplikasyonlar olan bir thalassemia major olgusu. Türkiye Klinikleri Pediatri, 2:205-208, 1993.
Arcasoy A, Turan F, Yeşil N, Kemahlı S, Canatan D, Uysal Z, Canatan D, Akar N: Muğla ili ve çevresinde thalassemia ve anormal hemoglobin sıklığının taraması. Pediatride Yönelişler, 1(2): 78-80, 1994
Kemahlı S, Canatan D, Erden İ, Aytaç S, Uysal Z, Akar N, Konkan R, Yücesan S, Barlas M, Dindar H, Cin Ş, Arcasoy A: Hemolitik anemilerde splenektomi sonrası tromboz. A.Ü. Tıp Fakültesi Mecmuası, 47:605-612, 1994.
Canatan D, Uysal Z, Kemahlı S, Gözdaşoğlu S, Cin Ş, Arcasoy A, Akar N: Fanconi’s aplastic anemia ( Presentation and treatment of 21 cases). Journal of Ankara Medical School, 16:1001-1007, 1994.
Canatan D, Kemahlı S, Cin Ş, Öcal G, Akar N, Arcasoy A: Hereditary elliptocytosis with growth hormone and gonadotropin deficiency. Journal of Ankara Medical School, 16:1019-1022, 1994.
Kemahlı S, Akar N, Öcal G: Faktör VII eksikliği ile birlikte olan bir Noonan sendromu. Pediatride Yönelişler, 1(7): 114-116, 1995.
Sipahi T, Akar N, Kemahlı S, Uysal Z, Cin Ş, Arcasoy A: Çocuklarda edinsel aplastik anemi ve tedavisi (22 olgunun değerlendirilmesi) Klinik Bilimler-Pediatride Yönelişler, 2:11-13, 1996.
Sipahi T, Kemahlı S, Kır M, Binnet M, Tuncer S, Cin Ş, Arcasoy A: Hemofilide radyonüklid sinovektomi: olgu sunusu. Klinik Bilimler-Pediatride Yönelişler, 2:47-48, 1996.
Yıldırmak Y, Kemahlı S, Canatan D, Arcasoy A, Cin Ş: Çocukluk yaşlarında otoimmün hemolitik anemiler. Klinik Bilimler-Pediatride Yönelişler, 2(7): 94-98, 1996.
Özdemir O, Gürsel T, Tangün Y, Dündar S, Yalçın A, Nişli G, Haspolat K, Kılınç Y, Ağaoğlu L, Patıroğlu T, Kemahlı S, Erduran E, Koçak R, Dinçer S, Canatan D, Yeşilipek A, Tanyer G, Özcan O, Tunalı A, Aydoğdu İ, Albayrak D: Turkish National Haemophilia Registry. Preliminary Report on Practice Pattern of Haemophilia Treatment. 1st National Haemophilia Congress, Ankara, 5-7 May 1997. Turkish Journal of Haematology, 14(3) Suppl, 3-8, 1997.
Kemahlı S: Comprehensive Management of Haemophilia. 1st National Haemophilia Congress, Ankara, 5-7 May 1997.  Turkish Journal of Haematology, 14(3) Suppl, 8-11, 1997
Tekin M, Kemahlı S, Trombopoetin  ve Trombopoez. Turkish Electronic Journal of Medicine, 1(1), 1997. (http://www.ato.org.tr/tejm.htm)
Kemahlı S: Çocuklarda tromboz profilaksisi ve antitrombotik tedavi. Prospekt, 2: 80-86, 1998.
Akar N, Kemahlı S, Akar E, Mısırlıoğlu M, Uysal Z, Canatan D, Cin Ş:Common genetic variants in patients with chronic hemolytic disease and post-splenectomy thrombotic events. Turkish Journal of Haematology, 16(1):41-42, 1999.
Pasin M, Fıçıcılar H, Tekin D, Tekin M, Yavuzer S, Akar N, Kemahlı S, Arcasoy A:  Beta-Thalassemia majorda trombosit fonksiyonlarına yeni bir yaklaşım. Ankara Üniversitesi Tıp Fakültesi Mecmuası, 1999,52(4):205-209.
Deda G, Askar N, Kemahlı S, Uysal S, Güven A, Kabakuş N, Karagöl U: Cerebrovascular accidents and the role of factor V mutation in children. Journal of Ankara Medical School, 1999,21:147-150
Kemahlı S: Hastane Transfüzyon Komiteleri. Klinik Gelişim, 14:138-140, 2001.
Cin Ş, Kemahlı S, Solaz N: Blood banking and transfusion medicine education in undergraduate medical students (A model proposal). Blood Banking And Transfusion Medicine, 2003; 1: 89-92.
Kemahlı S: Transfusion indications for acute anemias. Blood Banking and Transfusion Medicine, 2003; 1(Suppl. 1): S67-69.
Şimşek F, Öztürk G, Kemahlı S, Erbaş D, Hasanoğlu A: Oxidant and antioxidant status in beta thalassemia major patients. Ankara Üniversitesi Tıp Fakültesi Mecmuası, 2005; 58: 34-38.
Kemahlı A, Alper A: Probleme Dayalı Öğrenmeye Yönelik Tutum Ölçeği, Eğitim Bilimleri ve Uygulama, 2006;5:191-206.

 
 
 
 
 
 
 
 

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Publications

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Student Ratings For Vertical Integration Sessions In Clinical Clerkships

Journal Article ,
Student Ratings For Vertical Integration Sessions In Clinical Clerkships. (2018). Student Ratings For Vertical Integration Sessions In Clinical Clerkships. Tıp Eğitimi Dünyası 52 (52), 27-34, 2018.

Investigation of an algorithm for anti HCV EIA reactivity in blood donor screening in Turkey in the absence of nucleic acid amplification screening

Journal Article ,
Investigation of an algorithm for anti HCV EIA reactivity in blood donor screening in Turkey in the absence of nucleic acid amplification screening. (2017). Investigation of an algorithm for anti HCV EIA reactivity in blood donor screening in Turkey in the absence of nucleic acid amplification screening. Transfusion And Apheresis Science 56 (5), 732-737, 2017.

TIP EĞİTİMİ VE HEKİMLİK DİLİMİZ NASIL TÜRKÇELEŞTİ?

Journal Article ,
TIP EĞİTİMİ VE HEKİMLİK DİLİMİZ NASIL TÜRKÇELEŞTİ?. (2015). TIP EĞİTİMİ VE HEKİMLİK DİLİMİZ NASIL TÜRKÇELEŞTİ?. Tıp Eğitimi Dünyası 14 (44), 5-12, 2015.

Comparison of stored umbilical cord blood and adult donor blood: transfusio feasibility

Journal Article ,
Comparison of stored umbilical cord blood and adult donor blood: transfusio feasibility. (2012). Comparison of stored umbilical cord blood and adult donor blood: transfusio feasibility. Turkish Journal Of Hematology, 29, 233-241.

Core curriculum policiy analysis in medical education

Journal Article ,
Core curriculum policiy analysis in medical education. (2012). Core curriculum policiy analysis in medical education. Mededworld.

Comparison of stored umbilical cord blood and adult donor blood: transfusion feasibility

Journal Article ,
Comparison of stored umbilical cord blood and adult donor blood: transfusion feasibility. (2012). Comparison of stored umbilical cord blood and adult donor blood: transfusion feasibility. Turkish Journal Of Hematology 29 (3), 233, 2012.

Core curriculum policy analysis in medical education

Journal Article ,
Core curriculum policy analysis in medical education. (2012). Core curriculum policy analysis in medical education. Amee Mededpublish 1 (1), 2012.

80~ 210W/Mk het Nitride van Aluminium Ceramisch voor de Apparatuur Macht

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80~ 210W/Mk het Nitride van Aluminium Ceramisch voor de Apparatuur Macht. (2010). 80~ 210W/Mk het Nitride van Aluminium Ceramisch voor de Apparatuur Macht. Brazilian Journal Of Infectious Diseases 14 (1), 41-46, 2010.

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HBV, HCV and HIV seroprevalence among blood donors in Istanbul, Turkey: how effective are the changes in the national blood transfusion policies?. (2010). HBV, HCV and HIV seroprevalence among blood donors in Istanbul, Turkey: how effective are the changes in the national blood transfusion policies?. Brazilian Journal Of Infectious Diseases 14 (1), 41-46, 2010.

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The significance of repeat testing in Turkish blood donors screened with HBV, HCV and HIV immunoassays and the importance of S/CO ratios in the interpretation of HCV/HIV …. (2010). The significance of repeat testing in Turkish blood donors screened with HBV, HCV and HIV immunoassays and the importance of S/CO ratios in the interpretation of HCV/HIV …. Transfusion Medicine 20 (3), 152-159, 2010.

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Groene thee verticale stand Vffs verpakkingsmachine. (2010). Groene thee verticale stand Vffs verpakkingsmachine. Brazilian Journal Of Infectious Diseases 14 (1), 41-46, 2010.

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De gloednieuwe CNC Machine van de Draad EDM. (2010). De gloednieuwe CNC Machine van de Draad EDM. Brazilian Journal Of Infectious Diseases 14 (1), 41-46, 2010.

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Perceptions of students in different phases of Medicai education of educational environment: Ankara University Facuity of medicine

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Inhibitor screening for patients with hemophilia in Turkey. (2006). Inhibitor screening for patients with hemophilia in Turkey. Turk J Hematol 23 (1), 25-32, 2006.

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Beta talasemi major hastalarinda oksidan ve antioksidan düzeyleri. (2005). Beta talasemi major hastalarinda oksidan ve antioksidan düzeyleri. Ankara Üniversitesi Tıp Fakültesi Mecmuası 58 (1), 34-38, 2005.

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Hematology education in a problem-based curriculum. (2005). Hematology education in a problem-based curriculum. Hematology 10 (Sup1), 161-163, 2005.

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DAHİLİ BİLİMLER/MEDICAL SCIENCES. (2005). DAHİLİ BİLİMLER/MEDICAL SCIENCES. Journal Of Ankara University Faculty Of Medicine 58 (1), 2005.

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Platelet aggregation in term and preterm newborns. (2005). Platelet aggregation in term and preterm newborns. Pediatric Hematology And Oncology 22 (2), 139-145, 2005.

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Analysis of pediatric thrombotic patients in Turkey. (2004). Analysis of pediatric thrombotic patients in Turkey. Pediatric Hematology And Oncology 21 (7), 573-583, 2004.

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How we derived a core curriculum: from institutional to national—Ankara University experience. (2004). How we derived a core curriculum: from institutional to national—Ankara University experience. Medical Teacher 26 (4), 295-298, 2004.

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Molecular pathology of haemophilia B in Turkish patients: identification of a large deletion and 33 independent point mutations. (2003). Molecular pathology of haemophilia B in Turkish patients: identification of a large deletion and 33 independent point mutations. British Journal Of Haematology 120 (4), 656-659, 2003.

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Factor V Leiden and prothrombin gene 20210A variant in neonatal thromboembolism and in healthy neonates and adults: a study in a single center. (2003). Factor V Leiden and prothrombin gene 20210A variant in neonatal thromboembolism and in healthy neonates and adults: a study in a single center. Pediatric Hematology And Oncology 20 (8), 627-634, 2003.

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Two Rare Hemoglobin Variants in the Turkish Population (Hb G-Coushatta (B 22 (B4) GLU-ALA and Hb J Iran (B 77 (EF1) HIS-ASP). (2000). Two Rare Hemoglobin Variants in the Turkish Population (Hb G-Coushatta (B 22 (B4) GLU-ALA and Hb J Iran (B 77 (EF1) HIS-ASP). Turkish Journal Of Haematology: Official Journal Of Turkish Society Of …, 2000.

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Endothelin-1 and von Willebrand factor in pseudoxanthoma elasticum. (2000). Endothelin-1 and von Willebrand factor in pseudoxanthoma elasticum. Pediatric Nephrology (Berlin, Germany) 14 (8-9), 882-883, 2000.

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Radiographic atlas of skeletal development Radiographic atlas of skeletal development, 1959. (1999). Radiographic atlas of skeletal development Radiographic atlas of skeletal development, 1959. Pediatrics International: Official Journal Of The Japan Pediatric Society 41 …, 1999.

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Antiphospholipid antibody syndrome in a pediatric case. (1999). Antiphospholipid antibody syndrome in a pediatric case. Pediatric Research 45 (5), 767-767, 1999.

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Growth and adolescence Growth and adolescence, 1962. (1999). Growth and adolescence Growth and adolescence, 1962. Pediatrics International: Official Journal Of The Japan Pediatric Society 41 …, 1999.

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Recombinant human growth hormone treatment in children with thalassemia major. (1999). Recombinant human growth hormone treatment in children with thalassemia major. Pediatrics International 41 (6), 655-661, 1999.

Cerebrovascular accidents and the role of factor V mutation in children

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Cerebrovascular accidents and the role of factor V mutation in children. (1999). Cerebrovascular accidents and the role of factor V mutation in children. Journal Of Ankara Medical School 21 (3), 147-150, 1999.

Homozygous protein C deficiency with a double variant His 202 to Tyr and Ala 346 to Thr.

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Homozygous protein C deficiency with a double variant His 202 to Tyr and Ala 346 to Thr. (1998). Homozygous protein C deficiency with a double variant His 202 to Tyr and Ala 346 to Thr. Blood Coagulation & Fibrinolysis: An International Journal In Haemostasis …, 1998.

Thromboembolism in β-thalassemia major

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Thromboembolism in β-thalassemia major. (1998). Thromboembolism in β-thalassemia major. Acta Haematologica 100 (3), 166-166, 1998.

Hypercoagulability in children with thalassemia major

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Hypercoagulability in children with thalassemia major. (1997). Hypercoagulability in children with thalassemia major. Clinical And Applied Thrombosis/Hemostasis 3 (2), 129-132, 1997.

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Immunodeficiencies in children

What is immunodeficiency? What does it cause? How do you suspect from immunodeficiency? Is it congenital, hereditary or acquired? What types are there?     Case 1 (AT)     A problem-based learning case being discussed in class regards an immunodeficiency disorder involving a 12-year-old boy. Shortly after he began walking, he developed worsening instability and imbalance until he was eventually confined to a wheelchair at 9 years of age. Additionally, he developed oculocutaneous telangiectasias beginning at approximately 3 years of age. During the discussion of this patient’s case, it is added that such patients commonly have chronic sinopulmonary disease and also have a high incidence of malignancy, particularly lymphoreticular malignancies. What is the mechanism of action responsible for this patient’s condition?       (A) Absent respiratory burst     (B) Blocked lysosomal trafficking     (C) Defective DNA repair     (D) Defects in peroxisome function     (E) Impaired toll-like receptor signaling   Case 2: (WAS) A 26-month-old boy, the first child of nonconsanguineous parents, was previously diagnosed as chronic immune thrombocytopenic purpura. Hb 11.7 WBC 4000 Plt 40 000 He was referred to our clinic with recurrent bruising and petechial lesions since 3.5 months of age. He had received prednisolone and intravenous immunoglobulin treatments. He had accompanying  mild transient eczema together with early onset of thrombocytopenia and small platelets.   Case 3: (SCID) A seven months old male infant born of non-consanguineous marriage presented with recurrent oral ulcers, fever along with failure to thrive since 4 months. He had macular rash over face and chest since 1 month. He had been hospitalized for pneumonia 15 days back. He was a full term normal vaginal delivery and birth weight was 3.1 kg. His elder 2 sisters were completely asymptomatic. He had been immunized till date and milestones were normal. On examination, he had pallor with hypo-pigmented macules over neck and perianal region. On examination of oral cavity, tonsils were absent. On systemic examination, he had hepatosplenomegaly. Due to absent tonsils with recurrent infections and failure to thrive, he was suspected to be suffering from a Primary Immunodeficiency. His hemogram showed hemoglobin of 9.2 mg/dl with WBC count of 15,000/cumm [76% polymorphs, 8% Band Forms and 16% lymphocytes] with absolute lymphocyte count of 2400/cumm suggestive of lymphopenia and ESR of 12mm at end of 1 hour. His renal function test, liver function tests, urine and stool examination were normal. His urine culture was suggestive of candida albicans. X-Ray Chest revealed no thymic shadow. His HIV ELISA was negative. His serum immunoglobulins were all elevated [S. IgA = 100 mg/dl, S. IgG = 1426 mg/dl, S. IgM = 160 mg/dl] and CD panel by flow cytometry was suggestive of T- B+ NK- severe combined immunodeficiency most likely X-linked variant [CD3 = 20 cells/cumm, CD4 = 21 cells/cumm, CD8 = 24 cells/cumm, CD19 = 330 cells/cumm, CD20 = 437 cells/cumm, CD56 = 66 cells/cumm, CD16 = 630 cells/cumm]. He was treated with Intravenous Fluconazole and advised regarding Bone Marrow Transplant. In view of oral ulcers, skin rash along with hepatosplenomegaly he was suspected as a case of Graft versus host disease due to engraftment of maternal T cells. However it could not be confirmed by HLA testing as parents were not willing for the same.   Discussion   Severe combined immunodeficiency (SCID) is characterized by abnormal T and B cell function from birth. It is the severest of all congenital immunodeficiencies and unless immunologic reconstitution is achieved through bone marrow transplantation or enzyme replacement, death usually occurs by 2 years of age (1). Several types of SCID have been identified and clinically classified as T-B+ or T-B- SCID depending on affection of B cells. T cells and subsets are low to absent in all types. X linked SCID is the commonest form of SCID and patients present as T-B+ NK- SCID (decreased T cells, normal B cell quantity and low Non-Killer cells) as was seen in our patient. Males are affected. Affected infants present with frequent episodes of diarrhea, pneumonia, sepsis and cutaneous infections within first few months of life. Failure to thrive after infections is common. Viral infections such as Varicella, Measles, Parainfluenzae, CMV, Epstein Barr Virus and fungal infections such as Candida, Pneumocystis Carinii (PCP) are common. Our patient had a candidial urinary tract infection. BCG vaccine can lead to disseminated TB. Infants lack the ability to reject foreign tissue and hence are at risk for graft-versus-host disease from maternal immunocompetent T cells or from T cells in non-irradiated blood transfusion or allogenic bone marrow transplant. Thymus tissue is hypoplastic and hypoplasia of adenoids, tonsils and peripheral lymph nodes is seen as was seen in our patient. Investigations reveal profound lymphopenia with diminished serum immunoglobulins and no antibody formation following investigation. Antibody levels may initially be normal due to passively transferred maternal antibodies. Analysis of lymphocyte subpopulation helps to identify the type of SCID (3). Treatment consists of bone marrow transplant. Gene therapy with enzyme replacement is useful in ADA deficient SCID . Normal 0 false false false EN-GB X-NONE X-NONE /* Style Definitions */ table.MsoNormalTable {mso-style-name:"Table Normal"; mso-tstyle-rowband-size:0; mso-tstyle-colband-size:0; mso-style-noshow:yes; mso-style-priority:99; mso-style-parent:""; mso-padding-alt:0cm 5.4pt 0cm 5.4pt; mso-para-margin-top:0cm; mso-para-margin-right:0cm; mso-para-margin-bottom:10.0pt; mso-para-margin-left:0cm; line-height:115%; mso-pagination:widow-orphan; font-size:11.0pt; font-family:"Calibri","sans-serif"; mso-ascii-font-family:Calibri; mso-ascii-theme-font:minor-latin; mso-hansi-font-family:Calibri; mso-hansi-theme-font:minor-latin; mso-bidi-font-family:"Times New Roman"; mso-bidi-theme-font:minor-bidi; mso-fareast-language:EN-US;}

Immunodeficiencies in children

What is immunodeficiency? What does it cause? How do you suspect from immunodeficiency? Is it congenital, hereditary or acquired? What types are there?     Case 1 (AT)     A problem-based learning case being discussed in class regards an immunodeficiency disorder involving a 12-year-old boy. Shortly after he began walking, he developed worsening instability and imbalance until he was eventually confined to a wheelchair at 9 years of age. Additionally, he developed oculocutaneous telangiectasias beginning at approximately 3 years of age. During the discussion of this patient’s case, it is added that such patients commonly have chronic sinopulmonary disease and also have a high incidence of malignancy, particularly lymphoreticular malignancies. What is the mechanism of action responsible for this patient’s condition?       (A) Absent respiratory burst     (B) Blocked lysosomal trafficking     (C) Defective DNA repair     (D) Defects in peroxisome function     (E) Impaired toll-like receptor signaling   Case 2: (WAS) A 26-month-old boy, the first child of nonconsanguineous parents, was previously diagnosed as chronic immune thrombocytopenic purpura. Hb 11.7 WBC 4000 Plt 40 000 He was referred to our clinic with recurrent bruising and petechial lesions since 3.5 months of age. He had received prednisolone and intravenous immunoglobulin treatments. He had accompanying  mild transient eczema together with early onset of thrombocytopenia and small platelets.   Case 3: (SCID) A seven months old male infant born of non-consanguineous marriage presented with recurrent oral ulcers, fever along with failure to thrive since 4 months. He had macular rash over face and chest since 1 month. He had been hospitalized for pneumonia 15 days back. He was a full term normal vaginal delivery and birth weight was 3.1 kg. His elder 2 sisters were completely asymptomatic. He had been immunized till date and milestones were normal. On examination, he had pallor with hypo-pigmented macules over neck and perianal region. On examination of oral cavity, tonsils were absent. On systemic examination, he had hepatosplenomegaly. Due to absent tonsils with recurrent infections and failure to thrive, he was suspected to be suffering from a Primary Immunodeficiency. His hemogram showed hemoglobin of 9.2 mg/dl with WBC count of 15,000/cumm [76% polymorphs, 8% Band Forms and 16% lymphocytes] with absolute lymphocyte count of 2400/cumm suggestive of lymphopenia and ESR of 12mm at end of 1 hour. His renal function test, liver function tests, urine and stool examination were normal. His urine culture was suggestive of candida albicans. X-Ray Chest revealed no thymic shadow. His HIV ELISA was negative. His serum immunoglobulins were all elevated [S. IgA = 100 mg/dl, S. IgG = 1426 mg/dl, S. IgM = 160 mg/dl] and CD panel by flow cytometry was suggestive of T- B+ NK- severe combined immunodeficiency most likely X-linked variant [CD3 = 20 cells/cumm, CD4 = 21 cells/cumm, CD8 = 24 cells/cumm, CD19 = 330 cells/cumm, CD20 = 437 cells/cumm, CD56 = 66 cells/cumm, CD16 = 630 cells/cumm]. He was treated with Intravenous Fluconazole and advised regarding Bone Marrow Transplant. In view of oral ulcers, skin rash along with hepatosplenomegaly he was suspected as a case of Graft versus host disease due to engraftment of maternal T cells. However it could not be confirmed by HLA testing as parents were not willing for the same.   Discussion   Severe combined immunodeficiency (SCID) is characterized by abnormal T and B cell function from birth. It is the severest of all congenital immunodeficiencies and unless immunologic reconstitution is achieved through bone marrow transplantation or enzyme replacement, death usually occurs by 2 years of age (1). Several types of SCID have been identified and clinically classified as T-B+ or T-B- SCID depending on affection of B cells. T cells and subsets are low to absent in all types. X linked SCID is the commonest form of SCID and patients present as T-B+ NK- SCID (decreased T cells, normal B cell quantity and low Non-Killer cells) as was seen in our patient. Males are affected. Affected infants present with frequent episodes of diarrhea, pneumonia, sepsis and cutaneous infections within first few months of life. Failure to thrive after infections is common. Viral infections such as Varicella, Measles, Parainfluenzae, CMV, Epstein Barr Virus and fungal infections such as Candida, Pneumocystis Carinii (PCP) are common. Our patient had a candidial urinary tract infection. BCG vaccine can lead to disseminated TB. Infants lack the ability to reject foreign tissue and hence are at risk for graft-versus-host disease from maternal immunocompetent T cells or from T cells in non-irradiated blood transfusion or allogenic bone marrow transplant. Thymus tissue is hypoplastic and hypoplasia of adenoids, tonsils and peripheral lymph nodes is seen as was seen in our patient. Investigations reveal profound lymphopenia with diminished serum immunoglobulins and no antibody formation following investigation. Antibody levels may initially be normal due to passively transferred maternal antibodies. Analysis of lymphocyte subpopulation helps to identify the type of SCID (3). Treatment consists of bone marrow transplant. Gene therapy with enzyme replacement is useful in ADA deficient SCID . Normal 0 false false false EN-GB X-NONE X-NONE /* Style Definitions */ table.MsoNormalTable {mso-style-name:"Table Normal"; mso-tstyle-rowband-size:0; mso-tstyle-colband-size:0; mso-style-noshow:yes; mso-style-priority:99; mso-style-parent:""; mso-padding-alt:0cm 5.4pt 0cm 5.4pt; mso-para-margin-top:0cm; mso-para-margin-right:0cm; mso-para-margin-bottom:10.0pt; mso-para-margin-left:0cm; line-height:115%; mso-pagination:widow-orphan; font-size:11.0pt; font-family:"Calibri","sans-serif"; mso-ascii-font-family:Calibri; mso-ascii-theme-font:minor-latin; mso-hansi-font-family:Calibri; mso-hansi-theme-font:minor-latin; mso-bidi-font-family:"Times New Roman"; mso-bidi-theme-font:minor-bidi; mso-fareast-language:EN-US;}